Melanotic neuroectodermal tumour of infancy. A case report.
نویسنده
چکیده
Melanotic neuroectodermal tumour of infancy is a rare neoplasm of neural crest origin, predominantly affecting the anterior maxilla of infants. Treatment generally consists of surgical excision. Long-term follow-up is important since recurrence and malignant transformation have been reported. The literature about melanotic neuroectodermal tumour of infancy is reviewed and a case occurring in a 4-month old infant is presented.
منابع مشابه
تومور ملانوتیک نورواکتودرمال در فک بالای شیرخوار هفت ماهه: یک گزارش مورد
Background and Objectives: Melanotic neuroectodermal tumor of infancy (MNTI) is a rare, usually benign neoplasm of neural crest origin. MNTI usually arises in infants within the first year of life. The tumor is usually observed in head and neck areas especially in maxilla; however it has been reported in other areas such as hip, bone marrow, and ovary as well. It usually appears as a ...
متن کاملMelanotic neuroectodermal tumour of infancy.
Melanotic neuroectodermal tumour of infancy is an extremely rare neoplasm arising in newborns and young children, typically involving the face or cranium. A case arising from the maxilla, requiring extensive resection with a near-total maxillectomy, is presented. A thorough review of the literature on this unusual tumour is provided, with emphasis on prognostic factors and appropriate treatment.
متن کاملMelanotic Neuroectodermal Tumor of Infancy
Melanotic neuroectodermal tumor of infancy (MNETI) is also known as pigmented neuroectodermal tumor of infancy, melanotic prognoma, retinal anlage tumor, pigmented epulis of infancy and congenital melanocarcinoma. It is a rare neoplasm, occuring primarily in maxilla and mandible of infants. Till 1990 about 200 cases had been recorded in world literature(l,2). We report a case with this entity.
متن کاملMelanotic neuroectodermal tumour of infancy (progonoma) treated by radical maxillary surgery.
Two cases of melanotic neuroectodermal tumour of infancy (MNTI), otherwise known as melanotic progonoma, both arising from the maxilla are presented here. The two infants both presented within three months of each other and though clinically Burkitt's lymphoma was stated as a possible diagnosis, the correct diagnosis was made on biopsy specimens. Radical surgery consisting of wide resection of ...
متن کاملMelanotic Neuroectodermal Tumor of Infancy
Melanotic neuroectodermal tumor of infancy (MNTI) is a relatively uncommon osteolytic-pigmented neoplasm that primarily affects the jaws of newborn infants. Here, we are reporting a case of MNTI presented at the age of 12 years. The objective of this report is to review the incidence, presentation, investigation protocols, management options and outcomes.
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ورودعنوان ژورنال:
- Journal
دوره 57 2 شماره
صفحات -
تاریخ انتشار 1991